Morphea profunda, eosinophilic fasciitis, and disabling pansclerotic morphea of children are included in this group, but overlapping of the extent and depth of cutaneous involvement in these. Morphoea american spelling, morphea is characterised by an area of inflammation and fibrosis thickening and hardening of the skin due to increased collagen deposition. Pdf bearbeiten pdfeditor arbeitet direkt in ihrem browser. Ultrasonography as an auxiliary diagnostic tool for. Morphea profunda may thus present as a neuromuscular mimic, even in case of nonprogressive skin sclerosis. Myositis in morphea profunda is generally limited to one region, whereas inflammatory myopathies generally cause diffuse proximal muscle weakness and. Morphea profunda is a disorder of unknown etiology but has been described to occur following vaccination and in association with borrelia burgdorferi infection. Some authorities feel that linear morphea and progressive facial hemiatrophy parry romberg syndrome are related conditions.
Las lesiones son mas bien difusas y poco circunscritas o lineales. Morphea profunda presenting as a neuromuscular mimic. Morphea has different clinical features according to the subtype and stage of evolution of the disease. Morphea profunda is a rare subtype of localized scleroderma and it is difficult to evaluate the conditions of sclerotic changes at an early stage. A read is counted each time someone views a publication summary such as the title, abstract, and list of authors, clicks on a figure, or views or downloads the fulltext.
Pdf bearbeiten adobe acrobat dc adobe document cloud. Keine registrierung oder installation erforderlich. Morphea is diagnosed based on findings of skin examination and skin biopsy. Extensive morphea profunda with autoantibodies and benign. Morfea profunda morfea panesclerosante invalidante del nino. Patients with morphea do not have raynaud phenomenon fingers turning red, white, and blue with cold exposure, redness and swelling of both hands red puffy hands, changes in the blood vessels along the nail edge nailfold capillary changes, or tightening of the skin of the fingers sclerodactyly. Morphea profunda refers to inflammatory and sclerotic lesions that start primarily from the deep dermis, subcutaneous fat and fascia.
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